Papillomatosis cutis carcinoides
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Papillomatosis cutis carcinoides
Related Terms: Verrucous Carcinoma, Squamous Cell Carcinoma, Epithelioma cuniculatum, Carcinoma cuniculatum
Late stage lymphedema, also commonly referred to elephantstasis can present with additional skin complications. One of these is a rare condition called papillomatosis cutis carcinoides. In appearance, this is similar to elephantiasis nostras verrucosa, which we discussed in our previous article.
Description
The subcutaneous tissue becomes woody (intense fibrosis); venous flow is compromised and the dermal layers take on a cobblestone appearance from collagen placque. Small flesh colored or pink "bubbles" break out from the skin.
The important diagnostic tool to determine an accurate diagnosis, is a biopsy.
Papillomatosis cutis carcinoides accompanies both lymphatic filiarasis and extreme long term primary lymphedema.
Information availability in Engish is difficult to find.
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Diagnostic Images - Papillomatosis cutis carcinoides
http://images.google.com/images?q=Papil ... a=N&tab=wi
Diagnostic Image #2
http://altmeyer.informatik.uni-wuerzbur ... 88601t.jpg
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Verrucous Carcinoma
http://www.emedicine.com/derm/topic452.htm
Verrucous carcinoma (VC) is a low-grade cutaneous squamous carcinoma which often presents on the foot where it is known as carcinoma cuniculatum
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Epithelioma cuniculatum
Pub Med Links Page
http://www.ncbi.nlm.nih.gov/entrez/quer ... _uid=56941
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Carcinoma cuniculatum
Pub Med Links Page
http://www.ncbi.nlm.nih.gov/entrez/quer ... &DB=pubmed
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Congestive lymphostatic papillomatosis
Stoberl C, Partsch H.
Dermatologische Abteilung, KA-Rudolfstiftung Wien.
In seven patients with papillomatosis cutis in chronically congested lower extremities (lymphoedema, chronic venous insufficiency, chronic cardiac insufficiency) indirect lymphography revealed abnormalities of dermal lymph drainage. In four of these patients punch biopsies were taken from the papillomas. Microscopic examination revealed hyperplasia of the epidermis and dilated capillary-like vessels. Papillomatosis cutis in chronically congested lower extremities can be distinguished from pseudoepitheliomatose and carcinomatose alterations by both clinical and histological examination. Impaired local lymph transport seems to be the decisive trigger mechanism for the development of these papillomas.
PMID: 3220758 [PubMed - indexed for MEDLINE]
http://www.ncbi.nlm.nih.gov/entrez/quer ... =iconabstr
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Tumor form of lymphostatic papillomatosis of the skin
[Article in German]
Niederauer HH, Schultz-Ehrenburg U, Tiedjen KU.
Abteilung Allgemeine Dermatologie mit Schwerpunkt Histopathologie und Angiologie, Ruhr-Universitat im St. Josef-Hospital Bochum.
The case of a patient with two plantar papillomatous tumours that had had a relapsing course over 10 years is presented. The tumours were located on the right forefoot and the left great toe. Several operations were performed for different diagnoses, i.e. plantar verrucae, verrucous carcinoma and pyoderma vegetans. Histologically, the papillomas proved to be pseudocarcinomatous hyperplasias with multiple ectatic dermal lymph plexuses. Indirect lymphography revealed a circumscribed lymphatic dysplasia with cystic-ectatic cutaneous vessels within the tumour area. Draining lymphatic collectors were conspicuously reduced in number. Isotope lymphography showed a normal lymph transport rate from the foot to the groin. It is concluded that the circumscribed disturbance of lymphatic drainage is the decisive cause of the reactive papillomatous hyperplasia. Thus, these papillomas clinically resembling verrucous carcinoma represent the tumour variant of a papillomatosis cutis lymphostatica.
Publication Types:
Case Reports
PMID: 1917474 [PubMed - indexed for MEDLINE]
http://www.ncbi.nlm.nih.gov/entrez/quer ... =iconabstr
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